Heptadecanoyl-<wbr/>L-carnitine-<wbr/>d<sub>3</sub> (chloride) MaxSpec<sup>®</sup> Standard

Heptadecanoyl-L-carnitine-d3 (chloride) MaxSpec® Standard

CAT N°: 35459
Price:

100.00 85.00

Heptadecanoyl-L-carnitine-d3 is intended for use as an analytical standard for the quantification of heptadecanoyl-L-carnitine by GC- or LC-MS. Heptadecanoyl-L-carnitine is a long-chain acylcarnitine composed of heptadecanoic acid (Item No. 19722) and L-carnitine (Item No. 21489). Levels of heptadecanoyl-L-carnitine are increased in dried blood spots from neonates with propionic or methylmalonic acidemias, inborn errors of metabolism characterized by a deficiency in the activity of propionyl-CoA carboxylase or L-methylmaolnyl-CoA mutase or its cofactor 5-deoxyadenosylcobalamin, respectively.{50369}

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