3-Methylglutaconic Acid

3-Methylglutaconic Acid

CAT N°: 34055
Price:

From 129.00 109.65

3-Methylglutaconic acid (3-MGA) is a branched-chain organic acid and product of leucine catabolism.{62255} 3-MGA accumulates in 3-methylglutaconic aciduria, which is caused by an inborn error of leucine metabolism characterized by 3-MGA-CoA hydratase deficiency, leading to delayed development, hypoglycemia, metabolic acidosis, and neurological impairments.{58551,62255}

Territorial Availability: Available through Bertin Technologies only in France

  • Synonyms
    • 3-methyl-2-pentenedioic acid
  • Correlated keywords
    • NSC249232 MGACoA 3MGA 3MGC methyl glutaconic
  • Product Overview:
    3-Methylglutaconic acid (3-MGA) is a branched-chain organic acid and product of leucine catabolism.{62255} 3-MGA accumulates in 3-methylglutaconic aciduria, which is caused by an inborn error of leucine metabolism characterized by 3-MGA-CoA hydratase deficiency, leading to delayed development, hypoglycemia, metabolic acidosis, and neurological impairments.{58551,62255}

We also advise you